Case Series: Two Cases of Critical Pulmonary Artery Stenosis Focusing on the Timing of Diagnosis and Management

Authors

  • Dyahris Koentartiwi Department of Pediatrics Faculty of Medicine Universitas Brawijaya Malang
  • Ardhanis Ramadhanti Department of Pediatrics Faculty of Medicine Universitas Brawijaya Malang
  • Monica Damayani Susilo Department of Pediatrics Faculty of Medicine Universitas Brawijaya Malang

Keywords:

Critical pulmonary stenosis, early diagnosis, late intervention, percutaneous transcatheter balloon valvuloplasty

Abstract

Critical stenosis of the pulmonary valve in neonates is related to ductus-dependent pulmonary circulation. Percutaneous transcatheter balloon valvuloplasty (PTBV) is the treatment of choice for critical pulmonary stenosis. Unfortunately, many children in developing countries are usually diagnosed late and seldom get immediate care, which leads to delayed growth and development and, ultimately, higher morbidity and mortality. We present two cases of critical pulmonary artery stenosis in a 17-year-old boy and a 4-day-old girl who received PTBV procedures, but had different outcomes. We underline the importance of early diagnosis and intervention in critical pulmonary stenosis for the patient’s prognosis.

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Published

2024-08-30

Issue

Vol. 33 No. 2 (2024)

Section

Case Report

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