Pseudotumor Hemofilia, Suatu Komplikasi Hemofilia yang Jarang
DOI:
https://doi.org/10.21776/ub.jkb.2016.029.02.13Abstract
Pseudotumor adalah kista berisi darah pada jaringan lunak atau tulang. Satu sampai dua persen hemofilia berat menyebabkan pseudotumor, yang bisa berasal dari jaringan lunak atau pada subperiosteal atau area intraosseus. Pseudotumor jarang terjadi namun merupakan komplikasi hemofilia yang berbahaya. Kami laporkan kasus pseudotumor hemofilia pada seorang laki-laki 27 tahun dengan keluhan bengkak pada paha kanan yang muncul tiba-tiba, merata dari pangkal paha sampai lutut. Keluhan hilang timbul, bergantian pada kaki kanan kiri sejak 2002. Riwayat perdarahan yang sulit berhenti 15 tahun sebelumnya. Pemeriksaan MRI (magnetic resonansi imaging) menunjukkan massa intra muskular regio femur dekstra 1/3 proksimal hingga 1/3 tengah dan massa intra muskular regio femur sinistra 1/3 proksimal melibatkan kompartemen anterior dan bone marrow replacement. Didapatkan Hemofilia A sedang dengan APTT memanjang (faktor VIII 7%) pada pemeriksaan darah. Pasien membaik dengan terapi konservatif, yaitu pemberian faktor VIII.
Kata Kunci: Hemofilia A, pseudotumor hemofilia
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